Iran University of Medical Sciences
Hepatoblastoma is the most common primary hepaticmalignancy in children but pedunculated hepatoblastoma is an extremely rare entity. Accurate diagnosis can be challenging due to its extrahepatic location and possibly its thin peduncle, which is not easily identified in imaging . Here, we report a case of asymptomatic giant palpable pedunculated hepatoblastoma in the LUQ of a four month old male infant, initially suspected of neuroblastoma based on abdominal ultrasound findings. the final diagnosis of giant pedunculated hepatoblastoma was made based on the
abdominal CT scan and diagnosis was confirmed by percutaneous biopsy. Due to the size of the tumor, complete removal of the tumor was not initially possible. therefore, the patient was treated with several courses of chemotherapy . The tumor was shrunk and then cimpletely removed. The patient was treated and no complications were found in the 6 month follow up. The pedunculated hepatoblastoma is very rare but should be considered as a possibility in the case of a perihepatic mass in a pediatric patient .